Cesarean Delivery as a Method to Avoid Neonatal Infection in Genodermatosis
Keywords:
medical genetics, skin diseases, genodermatosis, bullous epidermolysis, lamellar ichthyosis.Abstract
Introduction: Genodermatoses presenting epidermal alterations from birth, such as epidermolysis bullosa and lamellar ichthyosis, constitute a risk for the development of neonatal infections.
Case report: Two cases are reported. These parents decided to reproduce, even knowing the genetic risks for their offspring. The pregnant women were followed up until the end of the pregnancy by a multidisciplinary team, when it was decided to performe cesarean section to avoid the risks of neonatal infection. Although in both cases the children had skin lesions from birth, corresponding to family genodermatosis, no neonatal infections were reported.
Conclusions: The cases are reported due to the importance of this procedure to avoid neonatal infections in this type of patients.
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